Desmoplastic Small Round Cell Tumor: A Case Report
Bhuwan Kumar *
Department of General Surgery, MAMC, New Delhi, India.
*Author to whom correspondence should be addressed.
Abstract
Desmoplastic small round cell tumour is a very rare, highly malignant abdominal neoplasm of mesenchymal origin. Its non-specific symptoms at presentation and poor prognosis with a five year survival rate of 15% despite treatment make it a big challenge to manage. We wish to discuss a case of a young 17-year old male with abdominal pain and a palpable lump which was eventually diagnosed with desmoplastic round cell tumour.
Keywords: Desmoplastic small round cell tumor, prognosis, survival rate, polyphenotypic differentiation